Brief Review: Budd-Chiari Syndrome in Iran

Abstract

Background:

 Budd-Chiari syndrome (BCS) is a rare syndrome caused by hepatic venous outflow obstruction. The etiology of BCS differs between western and eastern countries. This article is a review of all published articles in Iranian and international journals regarding different aspects of BCS (prevalence, etiology, and conventional treatments) in Iran.

Materials and Methods :

 In this review, by accessing Med-line and Iran-medex, we have analyzed all relevant articles of BCS. In Iranian and international journals, two original articles and five case reports have been published regarding diagnosis and treatment of BCS in Iran.

Results :

 Some Iranian articles have discussed BCS in Iran. According to these articles, nowadays it is not possible to estimate the prevalence and incidence of BCS in Iran, nor is it possible to define the underlying etiology.

Conclusion:

 The current overview of BCS treatment in Iran is unclear. However, it seems that angioplasty treatment for the removal of mechanical obstructions, such as web obstruction, has been developed in Iran and is generally accepted by Iranian physicians. Web obstruction, according to one Iranian article is the most common underlying cause of BCS among Iranian patients. The lack of available investigations about the status of BCS in Iran necessitates multi-center studies.